most common visual defect in BBS is "Red-Cone" dystrophy which is an atypical form of retinitis pigmentosa. Red-Cone dystrophy is diagnosed in 93% of BBS patients with most of them going blind before the age of thirty (1)
average age of registered blindness was 15.5 years making the retinitis pigmentosa in BBS far more rapid than in typical isolated retinitis pigmentosa
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